Changes in muscle tone â poor muscle tone, muscle tightness/tension Our 8 y/o daughter has very occasionally had breath that smells like maple syrup. Itâs when he wears his fleece ones to bed (clean) and by morning I can smell it on them. He actually still smells like that when his blood sugar is high. A Verified Doctor answered. But being tired all the time is certainly a symptom of diabetes. Also, for the last year or so, he has lost 3 lbs. It means the body cannot process certain amino acids (the "building blocks" of protein), causing a harmful build-up of substances in the blood and urine. It's happened about 3 or 4 times over the past year, as clearly as we can figure. Maple syrup urine disease (MSUD) is a rare, inherited metabolic disorder. It is managed through diet with severe protein restriction. According to his dr., he's 10% in height & weight on the growth charts. Charlie: Yeah. The condition is named for the sweet odor of the urine of untreated babies. I googled and I don't think I have maple syrup urine disease, especially since it's not my urine that smellsâ¦ Answer 11 of 19: So, I'm at my local bank today and the teller asks about my upcoming Canadian vacation. He never wants to eat and when he does eat, it's 2 or 3 bites and then he says he's full. Maple syrup urine disease (MSUD) is a condition in which the body is unable to break down certain proteins. Individuals with classic maple syrup urine disease have little or no enzyme activity (usually less than 2 % of normal). This causes a build-up of harmful levels of these substances in the blood. Maple syrup urine disease is a genetic disorder where a person cannot process certain proteins. Toddler Urine Smells Like Maple Syrup. I have let this machine run for hours . Typically the odor is fishy, but odor is very subjective and one person's "maple syrup" may be another's "fishy". Do you mysteriously smell maple syrup everywhere? The condition gets its name from the distinctive sweet odor of affected infants' urine, particularly prior to diagnosis and during times of acute illness. Answer 1 of 19: So, I'm at my local bank today and the teller asks about my upcoming Canadian vacation. Her urine smells normal - no sweet smell; her perspiration is not abnormal either. I donât know why something would smell like maple syrup in a house that is constructed like it is. Maple syrup smell: Okay this sounds strange Iâm sure but for a while Iâve noticed my sonâs pjâs smell like maple syrup in the mornings. Maple syrup urine disease (MSUD) is a rare but serious inherited condition. 1 decade ago. Holly. and we both said "like maple syrup." It doesn't always happen but now and then my daughter's pee smells really sweet, like maple syrup. He weighs 32 lbs. (This disorder got its name from this common symptom.) Maple syrup urine disease (MSUD) is a metabolic disorder that is genetically inherited 2. She has a dry diaper so its not that. I thought for a couple days that she was stinky but disregarded it. The genetic defect is so named after its tell-tale symptom of characteristic, sweet smeling body secretions like urine, sweat, and earwax that is oddly reminiscent of maple syrup. It smells like maple-syrup. Normally, our bodies break down protein foods such as â¦ Maple syrup smelling urine in children: Introduction. I know thereâs a newborn condition that causes urine to smell like that but Iâm sure we would have known if he had that by now! She asks if I need currency and I explain that I don't as I usually use my travel credit card instead. The type of Freon is R410A some say it a leak. I've noticed a couple of nights that Morgan smells like maple syrup. You probably donât have maple syrup urine disease because itâs a rare inherited disorder that affects an estimated 1 in 185,000 infants worldwide, according to the National Institutes of Health. It's hard to work out in public places because of this. Why does my child smell like maple syrup? Sluggish/slow/tiredness and weakness. » Review Causes of Maple syrup smelling urine in children: Causes My toddler smelling like syrup? Babies with the disease feed poorly, vomit, and have seizures and occasionally brain swelling. One morning I made my DH sniff it and he was like "smells like that fenugreek stuff you used to take." It still smells like maple syrup. If he is taking a lot of whey protein powder, he's getting a lot of branched-chain amino acids, and they have an odor of maple syrup. Poor feeding, vomiting, loss of appetite, irritability. Maple syrup smelling urine in children: Maple syrup smelling urine in children refers to a child's urine that smells like maple syrup. There are many instances when a weird or bad baby smell may indicate a health problem. Of course I just googled it and there's tons of info about Maple Syrup Urine Disease (which is very bad news if that's what it is). Joined: Jan 16, 2012 Messages: 9,368 Likes Received: 12,524 #1 ghostonvacation, Sep 15, 2012. These amino acids and their toxic byproducts build up in the blood and urine, resulting in symptoms such as lethargy, poor appetite, seizures, and vomiting. It causes an inability for the body to break down the amino acids valine, leucine and isoleucine. so I figured, if he can smell it too I'm going to look it up online. I've read about maple syrup urine disease or could be a sign of diabetes. It is an inherited disorder , and a parent may notice their baby or child has sweet-smelling urine. This leads to a buildup of these chemicals in the blood. The bedroom, the closet and the bathroom, so â¦ In children with MSUD, the body cannot break down certain amino acids, the building blocks of protein. I'm a 41 year old female and on several occasions in the past six months, I've noticed that I smell really sweet, almost a maple syrupy smell. This is a very weird smell for dogs and it stays on even if you thoroughly bath your dog applying some shampoos with fragrance as well. When I sweat my body odor smells like onions. Infants with this type of maple syrup urine disease will show symptoms within the first several days of life. A child can recover if diagnosed early and treated appropriately. Discussion in 'The Toddler Years(1-3)' started by i4get, May 29, 2008. i4get Well-Known Member. It is still blowing cold air. Add Friend Ignore [a k&m] 2 kids; Iowa 6968 posts. Rachel had maple syrup urine disease. These rare disorders are trimethylaminuria, maple syrup urine disease etc. Charlie: Well, itâs the bedroom-Tom: Those smell questions are tough. We live in a block of 4 town homes so thought, although weird maybe someone just made pancakes. My 2 year old has had this 'syrupy' sweet smell for about 6ish months now. Frequent shower does no good. Like in humans, Canine Diabetes is a serious condition. I'm hoping it's neither! People with this condition cannot break down the amino acids leucine, isoleucine, and valine. The disease prevents your body from breaking down certain amino acids. Maple syrup urine disease (MSUD) is an autosomal recessive metabolic disorder affecting branched-chain amino acids.It is one type of organic acidemia. Smell the toddler's breath, if it, too, smells sickly sweet like maple syrup, go to the doctor. Classic maple syrup urine disease is the most common type. Maple syrup urine disease (MSUD) is an inherited condition caused by a faulty gene. : i woke up to baby crying at 2am and i noticed her diaper smelled very sweet, almost like maple syrup. Any idea what could cause this? But it has persisted for a few days. I know it sounds weird, but my initial reaction to reading that was "oh, diabetes". See detailed information below for a list of 1 causes of Maple syrup smelling urine in children, including diseases and drug side effect causes. Dogsâ breath often smells funky, and a particularly bad stink can indicate serious illnesses like kidney disease and liver problems. Feb 25th '12. 2 0. It is caused by a defect in 1 of 3 genes. [a k&m] 2 kids; Iowa 6968 posts . A US doctor answered Learn more. Sometimes there is increased discharge. This is rare but is seen in some metabolic disorders. Baby's pee smelled like maple syrup? It is unusual for a healthy female on medicines to suddenly develop a body odor like maple syrup. Absolutely, but as far as that goes, Iâd investigate the walls. A scent of maple syrup may mean maple syrup urine disease a genetic disorder. Urine, sweat, or earwax that smells like maple syrup or burnt sugar. instead of gaining any weight. Maple syrup urine disease (MSUD) is inherited, which means it is passed down through families. Trichomonas causes similar odor, and other STDs like gonorrhea or chlamydia are more common in BV. Posted 03/11/2011. 1 doctor answer. Help! My Dogâs Breath Smells Like Maple Syrup. sweetypuffs. Want to know more about maple syrup urine disease and its symptoms? Now, when do weird or bad baby smells indicate a problem? Some dog owners show a lot of concern when their dog smells like maple syrup. Maple syrup urine disease is an extremely rare genetic disorder in a healthy individual certain enzymes breakdown amino acids found in protein-rich foods, but in patients like Rachel, those enzymes are absent, allowing the amino acids to wreak havoc on the brain. She is almost 7 weeks old and this is the first time I noticed this. So I google and find "maple syrup urine disease" and think THAT'S IT! For example, a musty odor can mean a rare but serious condition called Phenylketonuria. Overview. See a doctor soon to check it out. Page 1 of 3 1 2 3 Next > ghostonvacation Well-Known Member. She asks if I need currency and I explain that I don't as I usually use my travel credit card instead. MSUD is considered an amino acid condition because people with MSUD have trouble breaking down certain amino acids, the building blocks of proteins. A few days ago the wife and I came home and could smell a super sweet smell that reminded of us maple syrup. urine that smells like maple syrup or burnt sugar; Babies with MSUD have episodes of illness called metabolic crisis This is a serious health condition caused by low blood sugar and the build-up of toxic substances in the blood. Feb 25th '12. ! Discussion in 'General' started by ghostonvacation, Sep 15, 2012. Some dogs smell like corn chips, nachos and sometimes like body powder. what will cause your sweat/body odor to smell like maple syrup? All of my children have had this smell as toddlers and Ive always wondered why! my apartment smells like maple syrup. Maple syrup: Maple syrup urine disease occurs when the body can't process certain amino acids. ... obviously they found a portal that leads them to a maple syrup pool and they swim in it, get a giant pancake to float on, and so on. It seems to last all day, and to be coming from my skin! However, there is a common condition that results in sweet breath: Canine Diabetes. This may not always be present in all types.